What is the effect of cystic fibrosis on the respiratory and gastrointestinal systems?

What is the effect of cystic fibrosis on the respiratory and gastrointestinal systems?

CF causes thick mucus that clogs certain organs, such as the lungs, pancreas, and intestines. This may cause malnutrition, poor growth, frequent respiratory infections, breathing problems, and chronic lung disease.

How does cystic fibrosis affect the lungs?

Cystic fibrosis (CF) is an inherited disease that causes thickened mucus to form in the lungs, pancreas and other organs. In the lungs, this mucus blocks the airways, creating lung damage and making it hard to breathe.

What causes cystic fibrosis describe the pathophysiologic mechanisms of the disease?

Cystic fibrosis is caused by defects in the cystic fibrosis gene, which codes for a protein transmembrane conductance regulator (CFTR) that functions as a chloride channel and is regulated by cyclic adenosine monophosphate (cAMP).

How do you diagnose cystic fibrosis?

If you show symptoms of cystic fibrosis or your baby has a positive newborn screen for CF, a sweat test at a CF Foundation-accredited care center can help provide a CF diagnosis by measuring the concentration of salt in your or your baby’s sweat. The test is painless and is the most reliable way to diagnose CF.

What is hepatosplenomegaly?

Hepatosplenomegaly is a condition that causes swelling and enlargement of the liver and spleen. Medical conditions related to the liver often begin with the prefix “hepat-” (such as hepatitis) and “splen” refers to the spleen. The term “megaly” indicates that something is abnormally large.

How is hepatosplenomegaly diagnosed?

A blood test can help diagnose hepatosplenomegaly. A doctor will begin diagnosing hepatosplenomegaly by assessing a person’s medical history and current symptoms. A doctor will do a physical examination, paying specific attention to the abdomen for signs of organ enlargement.

What is the difference between jaundice and hepatosplenomegaly?

Jaundice is characterized by yellow skin or eyes. Hepatosplenomegaly occurs when the liver and spleen are much larger than their typical size. Usually, a person cannot feel the borders of their liver or spleen in their stomach. But if they have hepatosplenomegaly, they can typically feel these organs.

What are the treatments for hepatosplenomegaly?

Here are some tips for sticking with a healthy diet. Rest, hydration, and medication. Some less severe infections that lead to hepatosplenomegaly may be treated simply with appropriate medications and rest while making sure that you don’t become dehydrated.